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A Case of Vohwinkel's Syndrome Succesfully Treated with Acitretin

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dc.creator YILDIRIM, Mehmet
dc.creator Ceyhan, Ali Murat
dc.creator Akkaya, Vahide Baysal
dc.creator Calapoglu, Niluefer Sahin
dc.date 2009-11-30T22:00:00Z
dc.date.accessioned 2020-10-06T10:40:06Z
dc.date.available 2020-10-06T10:40:06Z
dc.identifier 7ef3445d-f6f7-41c4-bc97-2c5d2bcddecb
dc.identifier https://avesis.sdu.edu.tr/publication/details/7ef3445d-f6f7-41c4-bc97-2c5d2bcddecb/oai
dc.identifier.uri http://acikerisim.sdu.edu.tr/xmlui/handle/123456789/64568
dc.description Vohwinkel's syndrome (Keratoderma hereditaria mutilans) is a rare genodermatosis consisting of hyperkeratosis of the palms and soles with a characteristic "honeycomb" appearance, "starfish-shaped" keratotic plaques on the dorsum of hands and feet and fibrous constricting bands (pseudoainhum) at the interphalangeal joints Associated findings with the disease are cicatricial alopecia, ichthyosiform dermatoses, acoustic impairment, deafness, spastic paraplegia and myopathy, and nail anomalies Etretinate and isotretinoin have been used successfully in several patients with Vohwinkel's syndrome to reverse both the keratoderma and pseudoainhum in this report, we described a case with Vohwinkel's syndrome that presented with generalized ichthyosis, diffuse palmoplantar keratoderma, pseudoainhum, onychogryphosis, ectropion and bilateral sensorineural hearing loss and was successfully treated with acitretin, 35 mg/day orally. (Turkderm 2009; 43; 180-2)
dc.language tur
dc.rights info:eu-repo/semantics/closedAccess
dc.title A Case of Vohwinkel's Syndrome Succesfully Treated with Acitretin
dc.type info:eu-repo/semantics/article


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