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LIGNEOUS CONJUNCTIVITIS IN A DANDY-WALKER SYNDROME: A RARE CASE

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dc.creator DEMİR, Süleyman; UNIVERSITY OF HEALTH SCIENCES, GULHANE FACULTY OF MEDICINE
dc.creator ÖZGE, Gökhan; UNIVERSITY OF HEALTH SCIENCES, GULHANE FACULTY OF MEDICINE
dc.creator AYYILDIZ, Önder; UNIVERSITY OF HEALTH SCIENCES, GULHANE FACULTY OF MEDICINE
dc.date 2021-09-13T00:00:00Z
dc.date.accessioned 2021-12-03T11:47:03Z
dc.date.available 2021-12-03T11:47:03Z
dc.identifier https://dergipark.org.tr/tr/pub/sdutfd/issue/64881/806926
dc.identifier 10.17343/sdutfd.806926
dc.identifier.uri http://acikerisim.sdu.edu.tr/xmlui/handle/123456789/94240
dc.description Ligneous conjunctivitis is a disease usuallycharacterized by type 1 plasminogen deficiency. Aswell as being inherited, it may also be associatedwith infection or trauma. It is characterized by thewoody appearance of pseudo-membranes rich infibrin, especially seen in the tarsal conjunctiva. İnits treatment heparin, alpha chymotrypsin, topicalhyaluronidase, corticosteroids, cyclosporine, andsurgical excision of membranes exist. In this study, weaimed to demonstrate the association of hydrocephalusand ligneous conjunctivitis in a 10-month-old malepatient who had a ventricular-peritoneal shunt forhydrocephalus.
dc.description Lignöz konjoktivit, genellikle tip 1 plazminojen eksikliğiile karakterize bir hastalıktır. Genetik kalıtımlıolduğu gibi enfeksiyon veya travma ile de ilişkiliolabilir. Özellikle tarsal konjonktivada görülen odunsugörünümde fibrinden zengin psödomembranlarlakarakterizedir. Tedavisinde; heparin, alfa kimotripsin,topikal hiyalüronidaz, kortikosteroidler, siklosporin vemembranların cerrahi eksizyonu yer almaktadır. Buçalışmada, hidrosefali nedeniyle ventrikülo-peritonealşant uygulanmış 10 aylık erkek hastada Dandy-Walker spektrumuna bağlı hidrosefali ve lignözkonjonktivit birlikteliğini göstermek amaçlanmıştır.
dc.format application/pdf
dc.language tr
dc.publisher Süleyman Demirel Üniversitesi
dc.publisher Süleyman Demirel University
dc.relation https://dergipark.org.tr/tr/download/article-file/1332691
dc.source Volume: 28, Issue: 3 515-517 en-US
dc.source 1300-7416
dc.source 2602-2109
dc.source SDÜ Tıp Fakültesi Dergisi
dc.subject Ligneous conjunctivitis,Hydrocephalus,Dandy–Walker sydrome
dc.subject Lignöz Konjoktivit,Hidrosefali,Dandy-Walker Sendromu
dc.title LIGNEOUS CONJUNCTIVITIS IN A DANDY-WALKER SYNDROME: A RARE CASE en-US
dc.title YENİ DOĞANDA GÖRÜLEN LİGNÖZ KONJOKTİVİT VE DANDY-WALKER SENDROMU İLİŞKİSİ: NADİR BİR OLGU tr-TR
dc.type info:eu-repo/semantics/article
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